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Rev. otorrinolaringol. cir. cabeza cuello ; 73(1): 68-72, abr. 2013. ilus, tab
Article in Spanish | LILACS | ID: lil-679046

ABSTRACT

La amiloidosis asociada a diálisis es una patología causada por depósito de fibrillas amiloides constituidas por la proteína beta 2 microglobulina1-5. Es una complicación seria y excepcional que ocurre en pacientes sometidos a hemodiálisis de larga data. El caso que presentamos corresponde a un paciente de 56 años en hemodiálisis hace 36 añ os, con amiloidosis del conducto auditivo externo bilateral. Sólo 13 casos de amiloidosis en el conducto auditivo externo, incluido éste han sido reportados en la literatura66-14. Este corresponde al tercercaso de amiloidosis asociada a diálisis del conducto auditivo externo reportado en la literaturaf6,10.


Dialysis related amyloidosis is a disorder caused by deposition of amyloid fibrils formed by beta-2 microglobulin1-5. It is a serious and exceptional complication in patients undergoing longterm hemodialysis. The present case involved a 56 years old man who had been on hemodialysis for 36 years with bilateral amyloidosis of the external auditory canal. Only 13 cases of amyloidosis in the ear canal, including the present case have been reported in the literature66-14. This is the third reported case of dialysis related amyloidosis of the ear canal6,10.


Subject(s)
Humans , Male , Middle Aged , Renal Dialysis/adverse effects , Ear Diseases/etiology , Amyloidosis/etiology , Tomography, X-Ray Computed , Long-Term Care , Ear Canal/surgery , Ear Diseases/surgery , Ear Diseases/diagnosis , Amyloidosis/surgery , Amyloidosis/diagnosis , Kidney Failure, Chronic/complications , Kidney Failure, Chronic/therapy
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